| CASE REPORT |
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| Year : 2016 | Volume
: 10
| Issue : 3 | Page : 350-352 |
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Multiple pterygium syndrome: Challenge for anesthesiologist
P Sethi1, PK Bhatia1, N Gupta2, K Singh2
1 Department of Anesthesia and Critical Care, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India
2 Department of Pediatrics, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India
Correspondence Address:
P Sethi
Department of Anesthesia and Critical Care, All India Institute of Medical Sciences, Jodhpur - 342 005, Rajasthan
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/1658-354X.174901
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Multiple pterygium syndrome (MPS) is a very rare autosomal recessive disorder characterized by flexion of joint and digit contractures, skin webbing, cleft palate, deformity of the spine, and cervical spine fusion. Difficult airway is associated mainly due to micrognathia, retrognathia, webbing of the neck, and limitation of the mouth opening and neck extension. We are reporting a case of a 5-year-old female diagnosed with MPS and exhibiting a bilateral club foot and congenital vertical talus. The patient was posted for manipulation and above the knee casting under general anesthesia. |
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